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Video 1 Two-chamber view cine sequence of patient with Yamaguchi syndrome showing midventricular obstruction and apical aneurysm
Video 2 Four-chamber view cine sequence of patient with Yamaguchi syndrome showing midventricular obstruction and apical aneurysm
Video 3 Two-chamber view cine sequence of patient with hypertrophic cardiomyopathy and congenital diverticulum. Diverticular contractility is less evident as a visible inward motion but rather as a subtle early systolic increase in thickness
Video 4 Four-chamber view cine sequence of patient with hypertrophic cardiomyopathy and congenital diverticulum. Diverticular contractility is less evident as a visible inward motion but rather as a subtle early systolic increase in thickness
Opmerkingen
Video online
The online version of this article contains 4 videos. The article and the videos are online available (https://doi.org/10.1007/s12471-023-01852-6). The videos can be found in the article back matter as “Electronic Supplementary Material”.
Hypertrophic cardiomyopathy (HCM) can manifest as rare pouch-like anomalies in the left ventricle, such as congenital diverticula or aneurysms, which have significant clinical implications. We present two distinct cases of this type of HCM. First, we saw a 67-year-old man with an HCM-related apical aneurysm, known as Yamaguchi syndrome (Fig. 1a, and see Videos 1 and 2 in Electronic Supplementary Material). Second, there was a 50-year-old woman who had a congenital left ventricular diverticulum, which was diagnosed by cardiac magnetic resonance imaging (MRI) (Fig. 1b, and see Videos 3 and 4 in Electronic Supplementary Material). Concerns about the potential rupture risks associated with diverticula prompted her to opt for surgical correction. Discriminating between diverticula and aneurysms hinges on both morphological characteristics and contractility patterns. Notably, congenital diverticula, characterised by their extremely thin walls, only exhibit nuanced contractile behaviours. Cardiac MRI plays a pivotal role, as it distinctly identifies the scar-like alterations inherent to aneurysms, a feature absent in diverticula. While traditional HCM approaches guide aneurysm treatment, diverticulum management is case-specific, highlighting the need for further clinical research.
Fig. 1
Two-chamber late gadolinium enhancement image of a patient with Yamaguchi syndrome and apical aneurysm showing fibrotic apical aneurysm (yellow arrow) and b patient with hypertrophic cardiomyopathy and congenital diverticulum without evidence of fibrosis (red arrow)
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Conflict of interest
S. Quick, K. Ibrahim, A. Youssef and L. Payo-Anez declare that they have no competing interests.
Open Access This article is licensed under a Creative Commons Attribution 4.0 International License, which permits use, sharing, adaptation, distribution and reproduction in any medium or format, as long as you give appropriate credit to the original author(s) and the source, provide a link to the Creative Commons licence, and indicate if changes were made. The images or other third party material in this article are included in the article’s Creative Commons licence, unless indicated otherwise in a credit line to the material. If material is not included in the article’s Creative Commons licence and your intended use is not permitted by statutory regulation or exceeds the permitted use, you will need to obtain permission directly from the copyright holder. To view a copy of this licence, visit http://creativecommons.org/licenses/by/4.0/.
Het Netherlands Heart Journal wordt uitgegeven in samenwerking met de Nederlandse Vereniging voor Cardiologie. Het tijdschrift is Engelstalig en wordt gratis beschikbaa ...
Video 1 Two-chamber view cine sequence of patient with Yamaguchi syndrome showing midventricular obstruction and apical aneurysm
Video 2 Four-chamber view cine sequence of patient with Yamaguchi syndrome showing midventricular obstruction and apical aneurysm
Video 3 Two-chamber view cine sequence of patient with hypertrophic cardiomyopathy and congenital diverticulum. Diverticular contractility is less evident as a visible inward motion but rather as a subtle early systolic increase in thickness
Video 4 Four-chamber view cine sequence of patient with hypertrophic cardiomyopathy and congenital diverticulum. Diverticular contractility is less evident as a visible inward motion but rather as a subtle early systolic increase in thickness
Metagegevens
Titel
Aneurysm or diverticulum? You better look twice—Two rare faces of hypertrophic cardiomyopathy
Auteurs
Silvio Quick Karim Ibrahim Akram Youssef Lorena Payo-Anez
